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Cystic fibrosis
- ROCK STUDY in CF: sustained anti-inflammatory effects of lumacaftor–ivacaftor in sputum and peripheral blood samples of adult patients with cystic fibrosis—an observational studyParniya Arooj, David V Morrissy, Yvonne McCarthy, Tamara Vagg, Mairead McCarthy, Claire Fleming, Mary Daly, Joseph A Eustace, Desmond M Murphy, B J PlantBMJ Open Respiratory Research May 2023, 10 (1) e001590; DOI: 10.1136/bmjresp-2022-001590
- Feasibility of dynamic chest radiography to calculate lung volumes in adult people with cystic fibrosis: a pilot studyThomas Simon FitzMaurice, Caroline McCann, Dilip Nazareth, Scott Hawkes, Matthew Shaw, Paul Stephen McNamara, Martin WalshawBMJ Open Respiratory Research May 2023, 10 (1) e001309; DOI: 10.1136/bmjresp-2022-001309
- Registry-based study in people with cystic fibrosis and an R117H variant treated with ivacaftorMark Higgins, Thalia Farietta, Daniel Campbell, Meng Liu, Josh Ostrenga, Alexander Elbert, Judy Shih, Nataliya VolkovaBMJ Open Respiratory Research May 2023, 10 (1) e001447; DOI: 10.1136/bmjresp-2022-001447
- Prospectively evaluating maternal and fetal outcomes in the era of CFTR modulators: the MAYFLOWERS observational clinical trial study designRaksha Jain, Amalia Magaret, Phuong T Vu, Jill M VanDalfsen, Ashley Keller, Alexandra Wilson, Melissa S Putman, Nicole Mayer-Hamblett, Charles R Esther, Jennifer L Taylor-CousarBMJ Open Respiratory Research Jun 2022, 9 (1) e001289; DOI: 10.1136/bmjresp-2022-001289
- Integrating specialist palliative care to improve care and reduce suffering: cystic fibrosis (InSPIRe:CF) – study protocol for a multicentre randomised clinical trialJane Lowers, Elisabeth P Dellon, Anne Stephenson, Robert Arnold, Andrew Althouse, Kwonho Jeong, Ethan Dubin, Jesse Soodalter, Cade Hovater, Marie Bakitas, Jessica Goggin, William Hunt, Sigrid Ladores, Kimberly Curseen, Gretchen Winter, George Solomon, Jonathan Ailon, Douglas Conrad, Dio KavalieratosBMJ Open Respiratory Research Sep 2022, 9 (1) e001381; DOI: 10.1136/bmjresp-2022-001381
- Exploring the impact of elexacaftor-tezacaftor-ivacaftor treatment on opinions regarding airway clearance techniques and nebulisers: TEMPO a qualitative study in children with cystic fibrosis, their families and healthcare professionalsMaryam Almulhem, Nuala Harnett, Stephanie Graham, Iram Haq, Shelina Visram, Christopher Ward, Malcolm BrodlieBMJ Open Respiratory Research Oct 2022, 9 (1) e001420; DOI: 10.1136/bmjresp-2022-001420
- Porphyromonas, a potential predictive biomarker of Pseudomonas aeruginosa pulmonary infection in cystic fibrosisMarlène Keravec, Jérôme Mounier, Charles-Antoine Guilloux, Marie-Sarah Fangous, Stanislas Mondot, Sophie Vallet, Stéphanie Gouriou, Rozenn Le Berre, Gilles Rault, Claude Férec, Georges Barbier, Patricia Lepage, Geneviève Héry-ArnaudBMJ Open Respiratory Research Mar 2019, 6 (1) e000374; DOI: 10.1136/bmjresp-2018-000374
- Randomised cross-over trial evaluating the short-term effects of non-invasive ventilation as an adjunct to airway clearance techniques in adults with cystic fibrosisGemma Stanford, Helen Parrott, Diana Bilton, Penny Agent, Winston Banya, Nicholas SimmondsBMJ Open Respiratory Research Apr 2019, 6 (1) e000399; DOI: 10.1136/bmjresp-2018-000399
- CNS imaging studies in cystic fibrosis patients presenting with sudden neurological eventsSamantha Ellis, Catherine Rang, Tom Kotsimbos, Dominic Keating, Felicity Finlayson, Richard Stark, Dominic Thyagarajan, John WilsonBMJ Open Respiratory Research Aug 2019, 6 (1) e000456; DOI: 10.1136/bmjresp-2019-000456
- Timing of hypertonic saline and airway clearance techniques in adults with cystic fibrosis during pulmonary exacerbation: pilot data from a randomised crossover studyKatherine O'Neill, Fidelma Moran, Michael M Tunney, J Stuart Elborn, Ian Bradbury, Damian G Downey, Jackie Rendall, Judy M BradleyBMJ Open Respiratory Research Jan 2017, 4 (1) e000168; DOI: 10.1136/bmjresp-2016-000168
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