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Cystic fibrosis
- How can we relieve gastrointestinal symptoms in people with cystic fibrosis? An international qualitative surveySherie Smith, Nicola Rowbotham, Gwyneth Davies, Katie Gathercole, Sarah J Collins, Zoe Elliott, Sophie Herbert, Lorna Allen, Christabella Ng, Alan SmythBMJ Open Respiratory Research Sep 2020, 7 (1) e000614; DOI: 10.1136/bmjresp-2020-000614
- Intestinal current measurement and nasal potential difference to make a diagnosis of cases with inconclusive CFTR genetics and sweat testRebecca Minso, Angela Schulz, Christian Dopfer, Nadine Alfeis, Andrea van Barneveld, Lena Makartian-Gyulumyan, Gesine Hansen, Sibylle Junge, Carsten Müller, Felix C C Ringshausen, Annette Sauer-Heilborn, Frauke Stanke, Cornelia Stolpe, Stephanie Tamm, Tobias Welte, Anna-Maria Dittrich, Burkhard TümmlerBMJ Open Respiratory Research Oct 2020, 7 (1) e000736; DOI: 10.1136/bmjresp-2020-000736
- Investigating outcome measures for assessing airway clearance techniques in adults with cystic fibrosis: protocol of a single-centre randomised controlled crossover trialGemma Stanford, Jane C Davies, Omar Usmani, Winston Banya, Susan Charman, Mandy Jones, Nicholas J Simmonds, Diana BiltonBMJ Open Respiratory Research Oct 2020, 7 (1) e000694; DOI: 10.1136/bmjresp-2020-000694
- What effective ways of motivation, support and technologies help people with cystic fibrosis improve and sustain adherence to treatment?Rebecca J Calthorpe, Sherie J Smith, Nicola J Rowbotham, Paul A Leighton, Gwyneth Davies, Tracey Daniels, Katie Gathercole, Lorna Allen, Zoe C Elliott, Alan R SmythBMJ Open Respiratory Research Aug 2020, 7 (1) e000601; DOI: 10.1136/bmjresp-2020-000601
- Utility and validity of dynamic chest radiography in cystic fibrosis (dynamic CF): an observational, non-controlled, non-randomised, single-centre, prospective studyThomas Simon FitzMaurice, Paul Stephen McNamara, Dilip Nazareth, Caroline McCann, Ram Bedi, Matthew Shaw, Martin WalshawBMJ Open Respiratory Research Mar 2020, 7 (1) e000569; DOI: 10.1136/bmjresp-2020-000569
- Downregulation of epithelial sodium channel (ENaC) activity in human airway epithelia after low temperature incubationSangya Yadav, Ciaran A Shaughnessy, Pamela L Zeitlin, Preston E BratcherBMJ Open Respiratory Research Feb 2021, 8 (1) e000861; DOI: 10.1136/bmjresp-2020-000861
- Survival models to support shared decision-making about advance care planning for people with advanced stage cystic fibrosisNegin Hajizadeh, Meng Zhang, Meredith Akerman, Nina Kohn, Anna Mathew, Denis Hadjiliadis, Janice Wang, Martin L LesserBMJ Open Respiratory Research May 2021, 8 (1) e000794; DOI: 10.1136/bmjresp-2020-000794
- Variation in treatment preferences of pulmonary exacerbations among Australian and New Zealand cystic fibrosis physiciansGrace Currie, Anna Tai, Tom Snelling, André SchultzBMJ Open Respiratory Research Jul 2021, 8 (1) e000956; DOI: 10.1136/bmjresp-2021-000956
- Acceptability of patient reported outcome measures (PROMs) in a cystic fibrosis data registryIrushi Ratnayake, Susannah Ahern, Rasa RuseckaiteBMJ Open Respiratory Research Jul 2021, 8 (1) e000927; DOI: 10.1136/bmjresp-2021-000927
- Coil embolisation for massive haemoptysis in cystic fibrosisMartha Dohna, Diane Miriam Renz, Florian Stehling, Christian Dohna-Schwake, Sivagurunathan Sutharsan, Claus Neurohr, Hubert Wirtz, Olaf Eickmeier, Jörg Grosse-Onnebrink, Axel Sauerbrey, Volker Soditt, Krystyna Poplawska, Frank Wacker, Michael Johannes MontagBMJ Open Respiratory Research Aug 2021, 8 (1) e000985; DOI: 10.1136/bmjresp-2021-000985
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