Demographic | Patients (n=185) n (%) |
Mean age, years (SD) | 56.0 (13.1) |
Mean 6 min walk test, metres (SD) | 365 (146)* |
Mean incremental shuttle walk test, metres (SD) | 298 (198)* |
Gender | |
Male | 59 (32) |
Female | 126 (68) |
PH diagnosis | |
Idiopathic PAH | 66 (36) |
CTEPH | 20 (11) |
CTD PAH | 32 (18) |
Congenital PAH | 35 (19) |
Familial PH | 2 (1) |
Other | 6 (3) |
Unsure | 21 (12) |
Lives with | |
Family | 140 (76) |
Alone | 30 (16) |
Friends | 3 (2) |
Other | 11 (6) |
Employment | |
Full time | 17 (9) |
Part time | 26 (14) |
Not employed | 61 (34) |
Retired | 77 (43) |
WHO FC (patient reported) | |
Class I | 8 (5) |
Class II | 60 (34) |
Class III | 75 (42) |
Class IV | 34 (19) |
HADS-Anxiety score | |
0–7 | 360 (61) |
8–10 | 108 (18) |
11–14 | 89 (15) |
15–21 | 32 (5) |
HADS-Depression score | |
0–7 | 426 (73) |
8–10 | 103 (18) |
11–14 | 47 (8) |
15–21 | 11 (2) |
Oxygen | |
Not at all | 111 (61) |
Night-time only | 19 (10) |
As I need it | 25 (14) |
All of the time | 27 (15) |
Therapy | |
Single | 70 (39) |
Dual | 92 (51) |
Triple | 11 (6) |
No treatment | 7 (4) |
Nebuliser therapy | |
No | 165 (93) |
Yes | 13 (7) |
Subcutaneous therapy | |
No | 173 (97) |
Yes | 5 (3) |
Intravenous therapy | |
No | 173 (97) |
Yes | 5 (3) |
*Baseline values for the 6 min walk test and incremental shuttle walk test were missing in 31 and 10 patients, respectively.
CTD, connective tissue disease; CTEPH, chronic thromboembolic pulmonary hypertension; HADS, Hospital Anxiety and Depression Scale; PAH, pulmonary arterial hypertension; PH, pulmonary hypertension; WHO FC, WHO functional class.