Table 2

Diagnostic data and clinical characteristics collected at registry inclusion.

N=277
Diagnosis, n/N (%)
 Definite IPF257/277 (92.8)
 Probable IPF18/277 (6.5)
Diagnostic tests, n/N (%)
 HRCT270/277 (97.5)
 Chest X-ray120/277 (43.3)
 Bronchoalveolar lavage224/277 (80.9)
 Biopsy84/277 (30.3)
  Open surgical38/277 (13.7)
  VATS41/277 (14.8)
  Cryobiospy5/277 (1.8)
Clinical characteristics at inclusion
 Per cent predicted FVC,%*
  Mean (SD)80.6 (19.9)
  Median (range)78 (33­–154)
 Per cent predicted DLco, %†
  Mean (SD)46.9 (13.8)
  Median (range)46 (19−106)
 6MWD,m‡
  Mean (SD)426.2 (130.8)
  Median (range)420.5 (90–805)
 GAP Index, n/N, %
  I89/230 (38.7)
  II113/230 (40.8)
  III28/230 (10.1)
  • *n=230.

  • †n=221.

  • ‡n=92.

  • DLco, carbon monoxide diffusing capacity; FVC, forced vital capacity; GAP, Gender, Age, and Physiology; HRCT, high-resolution CT; IPF, idiopathic pulmonary fibrosis; 6MWD, 6 min walk distance; VATS, video-assisted thoracoscopic surgery.