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Interstitial Fibrosis
- Central lung gene expression associates with myofibroblast features in idiopathic pulmonary fibrosisYong Huang, Rob Guzy, Shwu-Fan Ma, Catherine A Bonham, Jonathan Jou, Jefree J Schulte, John S Kim, Andrew J Barros, Milena S Espindola, Aliya N Husain, Cory M Hogaboam, Anne I Sperling, Imre NothBMJ Open Respiratory Research Feb 2023, 10 (1) e001391; DOI: 10.1136/bmjresp-2022-001391
- National data on prevalence of idiopathic pulmonary fibrosis and antifibrotic drug use in Finnish specialised careJohanna Salonen, Minna Purokivi, Ulla Hodgson, Riitta KaarteenahoBMJ Open Respiratory Research Sep 2022, 9 (1) e001363; DOI: 10.1136/bmjresp-2022-001363
- Rationale and design of the SARCoidosis Outcomes in all respiratory Viral Infectious Diseases (SARCOVID) StudyRachel Strykowski, Divya C Patel, Manny Ribeiro Neto, Kerry M Hena, Mridu Gulati, LIsa A Maier, Karen PattersonBMJ Open Respiratory Research Jul 2022, 9 (1) e001254; DOI: 10.1136/bmjresp-2022-001254
- Diagnostic delay in IPF impacts progression-free survival, quality of life and hospitalisation ratesNils Hoyer, Thomas Skovhus Prior, Elisabeth Bendstrup, Saher Burhan ShakerBMJ Open Respiratory Research Jul 2022, 9 (1) e001276; DOI: 10.1136/bmjresp-2022-001276
- Antibody responses and risk factors associated with impaired immunological outcomes following two doses of BNT162b2 COVID-19 vaccination in patients with chronic pulmonary diseasesZitta Barrella Harboe, Sebastian Rask Hamm, Laura Pérez-Alós, Pradeesh Sivapalan, Helene Priemé, Torgny Wilcke, Peter Kjeldgaard, Saher Shaker, Alexander Svorre Jordan, Dina Leth Møller, Line Dam Heftdal, Johannes Roth Madsen, Rafael Bayarri-Olmos, Cecilie Bo Hansen, Mia Marie Pries-Heje, Rasmus Bo Hasselbalch, Kamille Fogh, Jose Juan Almagro Armenteros, Linda Hilsted, Erik Sørensen, Birgitte Lindegaard, Andrea Browatzki, Tor Biering-Sørensen, Ruth Frikke-Schmidt, Sisse Rye Ostrowski, Kasper Karmark Iversen, Henning Bundgaard, Susanne Dam Nielsen, Peter Garred, Jens-Ulrik Stæhr JensenBMJ Open Respiratory Research Jul 2022, 9 (1) e001268; DOI: 10.1136/bmjresp-2022-001268
- Study design and rationale for the TETON phase 3, randomised, controlled clinical trials of inhaled treprostinil in the treatment of idiopathic pulmonary fibrosisSteven D Nathan, Jurgen Behr, Vincent Cottin, Lisa Lancaster, Peter Smith, CQ Deng, Natalie Pearce, Heidi Bell, Leigh Peterson, Kevin R FlahertyBMJ Open Respiratory Research Jul 2022, 9 (1) e001310; DOI: 10.1136/bmjresp-2022-001310
- Neutrophil lymphocyte ratio as an indicator for disease progression in Idiopathic Pulmonary FibrosisAndrew Achaiah, Amila Rathnapala, Andrea Pereira, Harriet Bothwell, Kritica Dwivedi, Rosie Barker, Valentina Iotchkova, Rachel Benamore, Rachel K Hoyles, Ling-Pei HoBMJ Open Respiratory Research Jun 2022, 9 (1) e001202; DOI: 10.1136/bmjresp-2022-001202
- Correlation of respiratory oscillometry with CT image analysis in a prospective cohort of idiopathic pulmonary fibrosisJoyce K Y Wu, Jin Ma, Lena Nguyen, Emily Leah Dehaas, Anastasiia Vasileva, Ehren Chang, Jady Liang, Qian Wen Huang, Antonio Cassano, Matthew Binnie, Shane Shapera, Jolene Fisher, Clodagh M Ryan, Micheal Chad McInnis, Zoltán Hantos, Chung-Wai ChowBMJ Open Respiratory Research Apr 2022, 9 (1) e001163; DOI: 10.1136/bmjresp-2021-001163
- Responsiveness and meaningful change thresholds of the Living with Pulmonary Fibrosis (L-PF) questionnaire Dyspnoea and Cough scores in patients with progressive fibrosing interstitial lung diseasesJeffrey J Swigris, Donald M Bushnell, Klaus Rohr, Heiko Mueller, Michael Baldwin, Yoshikazu InoueBMJ Open Respiratory Research Mar 2022, 9 (1) e001167; DOI: 10.1136/bmjresp-2021-001167
- CC-90001, a c-Jun N-terminal kinase (JNK) inhibitor, in patients with pulmonary fibrosis: design of a phase 2, randomised, placebo-controlled trialZoran Popmihajlov, Donna J Sutherland, Gerald S Horan, Atalanta Ghosh, David A Lynch, Paul W Noble, Luca Richeldi, Theodore F Reiss, Steven GreenbergBMJ Open Respiratory Research Jan 2022, 9 (1) e001060; DOI: 10.1136/bmjresp-2021-001060
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