Clinical review: idiopathic pulmonary fibrosis--past, present and future

Respir Med. 2006 Nov;100(11):1871-85. doi: 10.1016/j.rmed.2006.08.017. Epub 2006 Sep 20.

Abstract

Idiopathic pulmonary fibrosis (IPF) is an important, and devastating, interstitial lung disease. It has a median mortality of only 3 years, worse than many cancers, and its incidence continues to rise. In this article, an overview of key developments in our understanding and clinical management of IPF will be provided.

Publication types

  • Review

MeSH terms

  • Administration, Oral
  • Adrenal Cortex Hormones / administration & dosage
  • Anti-Inflammatory Agents / administration & dosage
  • Combined Modality Therapy
  • Cortisone / administration & dosage
  • Humans
  • Prognosis
  • Pulmonary Fibrosis / diagnosis
  • Pulmonary Fibrosis / epidemiology
  • Pulmonary Fibrosis / therapy*

Substances

  • Adrenal Cortex Hormones
  • Anti-Inflammatory Agents
  • Cortisone