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Cystic fibrosis
- Registry-based study in people with cystic fibrosis and an R117H variant treated with ivacaftorMark Higgins, Thalia Farietta, Daniel Campbell, Meng Liu, Josh Ostrenga, Alexander Elbert, Judy Shih, Nataliya VolkovaBMJ Open Respiratory Research May 2023, 10 (1) e001447; DOI: 10.1136/bmjresp-2022-001447
- Feasibility of dynamic chest radiography to calculate lung volumes in adult people with cystic fibrosis: a pilot studyThomas Simon FitzMaurice, Caroline McCann, Dilip Nazareth, Scott Hawkes, Matthew Shaw, Paul Stephen McNamara, Martin WalshawBMJ Open Respiratory Research May 2023, 10 (1) e001309; DOI: 10.1136/bmjresp-2022-001309
- ROCK STUDY in CF: sustained anti-inflammatory effects of lumacaftor–ivacaftor in sputum and peripheral blood samples of adult patients with cystic fibrosis—an observational studyParniya Arooj, David V Morrissy, Yvonne McCarthy, Tamara Vagg, Mairead McCarthy, Claire Fleming, Mary Daly, Joseph A Eustace, Desmond M Murphy, B J PlantBMJ Open Respiratory Research May 2023, 10 (1) e001590; DOI: 10.1136/bmjresp-2022-001590
- Exploring the impact of elexacaftor-tezacaftor-ivacaftor treatment on opinions regarding airway clearance techniques and nebulisers: TEMPO a qualitative study in children with cystic fibrosis, their families and healthcare professionalsMaryam Almulhem, Nuala Harnett, Stephanie Graham, Iram Haq, Shelina Visram, Christopher Ward, Malcolm BrodlieBMJ Open Respiratory Research Oct 2022, 9 (1) e001420; DOI: 10.1136/bmjresp-2022-001420
- Integrating specialist palliative care to improve care and reduce suffering: cystic fibrosis (InSPIRe:CF) – study protocol for a multicentre randomised clinical trialJane Lowers, Elisabeth P Dellon, Anne Stephenson, Robert Arnold, Andrew Althouse, Kwonho Jeong, Ethan Dubin, Jesse Soodalter, Cade Hovater, Marie Bakitas, Jessica Goggin, William Hunt, Sigrid Ladores, Kimberly Curseen, Gretchen Winter, George Solomon, Jonathan Ailon, Douglas Conrad, Dio KavalieratosBMJ Open Respiratory Research Sep 2022, 9 (1) e001381; DOI: 10.1136/bmjresp-2022-001381
- Prospectively evaluating maternal and fetal outcomes in the era of CFTR modulators: the MAYFLOWERS observational clinical trial study designRaksha Jain, Amalia Magaret, Phuong T Vu, Jill M VanDalfsen, Ashley Keller, Alexandra Wilson, Melissa S Putman, Nicole Mayer-Hamblett, Charles R Esther, Jennifer L Taylor-CousarBMJ Open Respiratory Research Jun 2022, 9 (1) e001289; DOI: 10.1136/bmjresp-2022-001289
- Burden of cystic fibrosis in children <12 years of age prior to the introduction of CFTR modulator therapiesKathryn Bresnick, Emilio Arteaga-Solis, Stefanie J Millar, Glen Laird, Cecile LeCamusBMJ Open Respiratory Research Dec 2021, 8 (1) e000998; DOI: 10.1136/bmjresp-2021-000998
- Novel method to select meaningful outcomes for evaluation in clinical trialsCharlie McLeod, Richard Norman, Jamie Wood, Siobhain Mulrennan, Sue Morey, André Schultz, Mitch Messer, Kate Spaapen, Matthew Stoneham, Yue Wu, Alan Smyth, Christopher Blyth, Steve Webb, Steven Mascaro, Owen Woodberry, Tom SnellingBMJ Open Respiratory Research Oct 2021, 8 (1) e000877; DOI: 10.1136/bmjresp-2021-000877
- Coil embolisation for massive haemoptysis in cystic fibrosisMartha Dohna, Diane Miriam Renz, Florian Stehling, Christian Dohna-Schwake, Sivagurunathan Sutharsan, Claus Neurohr, Hubert Wirtz, Olaf Eickmeier, Jörg Grosse-Onnebrink, Axel Sauerbrey, Volker Soditt, Krystyna Poplawska, Frank Wacker, Michael Johannes MontagBMJ Open Respiratory Research Aug 2021, 8 (1) e000985; DOI: 10.1136/bmjresp-2021-000985
- Acceptability of patient reported outcome measures (PROMs) in a cystic fibrosis data registryIrushi Ratnayake, Susannah Ahern, Rasa RuseckaiteBMJ Open Respiratory Research Jul 2021, 8 (1) e000927; DOI: 10.1136/bmjresp-2021-000927
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