You are here
- Home
- topic
- BMJ Open Respiratory Research
- BMJ Open Respiratory Research
- Cystic fibrosis
Cystic fibrosis
- Exploring the impact of elexacaftor-tezacaftor-ivacaftor treatment on opinions regarding airway clearance techniques and nebulisers: TEMPO a qualitative study in children with cystic fibrosis, their families and healthcare professionalsMaryam Almulhem, Nuala Harnett, Stephanie Graham, Iram Haq, Shelina Visram, Christopher Ward, Malcolm BrodlieBMJ Open Respiratory Research Oct 2022, 9 (1) e001420; DOI: 10.1136/bmjresp-2022-001420
- Integrating specialist palliative care to improve care and reduce suffering: cystic fibrosis (InSPIRe:CF) – study protocol for a multicentre randomised clinical trialJane Lowers, Elisabeth P Dellon, Anne Stephenson, Robert Arnold, Andrew Althouse, Kwonho Jeong, Ethan Dubin, Jesse Soodalter, Cade Hovater, Marie Bakitas, Jessica Goggin, William Hunt, Sigrid Ladores, Kimberly Curseen, Gretchen Winter, George Solomon, Jonathan Ailon, Douglas Conrad, Dio KavalieratosBMJ Open Respiratory Research Sep 2022, 9 (1) e001381; DOI: 10.1136/bmjresp-2022-001381
- Prospectively evaluating maternal and fetal outcomes in the era of CFTR modulators: the MAYFLOWERS observational clinical trial study designRaksha Jain, Amalia Magaret, Phuong T Vu, Jill M VanDalfsen, Ashley Keller, Alexandra Wilson, Melissa S Putman, Nicole Mayer-Hamblett, Charles R Esther, Jennifer L Taylor-CousarBMJ Open Respiratory Research Jun 2022, 9 (1) e001289; DOI: 10.1136/bmjresp-2022-001289
- Burden of cystic fibrosis in children <12 years of age prior to the introduction of CFTR modulator therapiesKathryn Bresnick, Emilio Arteaga-Solis, Stefanie J Millar, Glen Laird, Cecile LeCamusBMJ Open Respiratory Research Dec 2021, 8 (1) e000998; DOI: 10.1136/bmjresp-2021-000998
- Novel method to select meaningful outcomes for evaluation in clinical trialsCharlie McLeod, Richard Norman, Jamie Wood, Siobhain Mulrennan, Sue Morey, André Schultz, Mitch Messer, Kate Spaapen, Matthew Stoneham, Yue Wu, Alan Smyth, Christopher Blyth, Steve Webb, Steven Mascaro, Owen Woodberry, Tom SnellingBMJ Open Respiratory Research Oct 2021, 8 (1) e000877; DOI: 10.1136/bmjresp-2021-000877
- Coil embolisation for massive haemoptysis in cystic fibrosisMartha Dohna, Diane Miriam Renz, Florian Stehling, Christian Dohna-Schwake, Sivagurunathan Sutharsan, Claus Neurohr, Hubert Wirtz, Olaf Eickmeier, Jörg Grosse-Onnebrink, Axel Sauerbrey, Volker Soditt, Krystyna Poplawska, Frank Wacker, Michael Johannes MontagBMJ Open Respiratory Research Aug 2021, 8 (1) e000985; DOI: 10.1136/bmjresp-2021-000985
- Acceptability of patient reported outcome measures (PROMs) in a cystic fibrosis data registryIrushi Ratnayake, Susannah Ahern, Rasa RuseckaiteBMJ Open Respiratory Research Jul 2021, 8 (1) e000927; DOI: 10.1136/bmjresp-2021-000927
- Variation in treatment preferences of pulmonary exacerbations among Australian and New Zealand cystic fibrosis physiciansGrace Currie, Anna Tai, Tom Snelling, André SchultzBMJ Open Respiratory Research Jul 2021, 8 (1) e000956; DOI: 10.1136/bmjresp-2021-000956
- Survival models to support shared decision-making about advance care planning for people with advanced stage cystic fibrosisNegin Hajizadeh, Meng Zhang, Meredith Akerman, Nina Kohn, Anna Mathew, Denis Hadjiliadis, Janice Wang, Martin L LesserBMJ Open Respiratory Research May 2021, 8 (1) e000794; DOI: 10.1136/bmjresp-2020-000794
- Downregulation of epithelial sodium channel (ENaC) activity in human airway epithelia after low temperature incubationSangya Yadav, Ciaran A Shaughnessy, Pamela L Zeitlin, Preston E BratcherBMJ Open Respiratory Research Feb 2021, 8 (1) e000861; DOI: 10.1136/bmjresp-2020-000861
Pages
- BMJ Open Respiratory Research
- Cough (3)
- Critical care (8)
- Cystic fibrosis (3)
- Lung cancer (9)
- Sleep (2)
- Thoracic surgery (1)
- Tuberculosis (2)